Microangiopatía trombótica como complicación de una pancreatitis aguda

  • Bruno Scarlatto Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Cátedra de Medicina Intensiva, Asistente. Médico Intensivista. MUCAM, Unidad de Medicina Intensiva, Médico de staff
  • Sofía Kohn Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Cátedra de Medicina Intensiva, Medicina Intensiva, Residente
  • William Manzanares Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Cátedra de Medicina Intensiva, Profesor Titular. Médico Intensivista. MUCAM, Unidad de Medicina Intensiva, Director
Palabras clave: PANCREATITIS AGUDA, PÚRPURA TROMBOCITOPÉNICA TROMBÓTICA

Resumen

La púrpura trombótica trombocitopénica (PTT) es una microangiopatía trombótica poco frecuente, que se caracteriza por anemia hemolítica y plaquetopenia, con una elevada morbimortalidad. Su forma más frecuente es la PTT inmune, también denominada adquirida, provocada por la deficiencia de la enzima disintegrin-like and metalloprotease with thrombospondin type 1 motif 13 (ADAMTS13) secundaria a la presencia en plasma de autoanticuerpos. Presentamos el caso de un paciente con diagnóstico de pancreatitis aguda (PA) complicada con PTT, asociación de presentación excepcional en la práctica clínica.

Citas

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Publicado
2022-12-20
Cómo citar
1.
Scarlatto B, Kohn S, Manzanares W. Microangiopatía trombótica como complicación de una pancreatitis aguda. Rev. Méd. Urug. [Internet]. 20 de diciembre de 2022 [citado 29 de marzo de 2024];38(4):e38412. Disponible en: http://www2.rmu.org.uy/ojsrmu311/index.php/rmu/article/view/988