Leiomyosarcoma of the inferior vena cava, reconstruction with interposition of prosthesis and anticoagulation

  • Alison Guillén Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Clínica Quirúrgica, Residente
  • Nicolás Tarigo Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Clínica Quirúrgica F, Profesor Adjunto
  • Mariana Zeoli Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Clínica Quirúrgica F, Asistente
  • Federico Cabo Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Catedra de Imagenología, Asistente
  • Gustavo Andreoli Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Clínica Quirúrgica F, Profesor Agregado
  • Roberto Valiñas Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Clínica Quirúrgica F, Profesor Director
Keywords: LEIOMYOSARCOMA, PROSTHESES AND IMPLANTS, INFERIOR VENA CAVA

Abstract

Primary leiomyosarcoma of the vena cava is a very rare neoplasm that originates from the smooth muscle cells of the tunica media. It represents 2% of all the leiomyosarcomas and 60% of the vena cava tumors. We report a case of 64-year-old patient consulting for a lower right back pain. The computed tomography shows a large retroperitoneal mass which encompasses the inferior vena cava and involves of right kidney. The surgical treatment of tumor resection is performed with right nephrectomy and interposition of Dacron prosthesis. The anatomopathological study shows a high-grade leiomyosarcoma, not compromising the renal capsule, with resection free. Radical resection with negative margins currently offers the best survival rate. Anticoagulation treatment for patients with prosthesis placement is still under discussion.

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Published
2023-06-20
How to Cite
1.
Guillén A, Tarigo N, Zeoli M, Cabo F, Andreoli G, Valiñas R. Leiomyosarcoma of the inferior vena cava, reconstruction with interposition of prosthesis and anticoagulation. Rev. Méd. Urug. [Internet]. 2023Jun.20 [cited 2024May14];39(2):e702. Available from: http://www2.rmu.org.uy/ojsrmu311/index.php/rmu/article/view/1033

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